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Titre du document / Document title

Papular elastorrhexis: a distinct variant of connective tissue nevi or an incomplete form of Buschke-Ollendorff syndrome?

Auteur(s) / Author(s)

CHOONHAKARN C. (1) ; JIRARATTANAPOCHAI K. (1) ;

Affiliation(s) du ou des auteurs / Author(s) Affiliation(s)

(1) Division of Dermatology, Department of Medicine, Faculty of Medicine, Srinagarind Hospital Medical School, Khon Kaen University, THAILANDE

Résumé / Abstract

Papular elastorrhexis is a rare entity, possibly a form of multiple elastic tissue naevi. The cutaneous lesions in this disorder are characterized by multiple white papules usually occurring on the trunk. These tend to be nonfollicular and scattered evenly over the affected area. Histopathologically, there is a decrease of elastic fibres, that may also appear thin and fragmented. Most reported cases are sporadic but familial occurrence has been described and some authors believe that papular elastorrhexis may represent a mild form of Buschke-Ollendorff syndrome. We report an 18-year-old woman whose clinical and histopathological features were compatible with papular elastorrhexis. There was no evidence of skeletal changes or relevant family history.

Revue / Journal Title

Clinical and experimental dermatology    ISSN  0307-6938   CODEN CEDEDE 

Source / Source

2002, vol. 27, no6, pp. 454-457 [4 page(s) (article)] (12 ref.)

Langue / Language

Anglais

Editeur / Publisher

Wiley-Blackwell, Oxford, ROYAUME-UNI  (1976) (Revue)

Mots-clés anglais / English Keywords

Genetic disease

;

Osteochondrodysplasia

;

Diseases of the osteoarticular system

;

Skin disease

;

Human

;

Asia

;

Buschke Ollendorff syndrome

;

Adolescent

;

Case study

;

Dermatofibrosis lenticularis

;

Thailand

;

Osteopoikilosis

;

Nevus

;

Mots-clés français / French Keywords

Maladie héréditaire

;

Ostéochondrodysplasie

;

Système ostéoarticulaire pathologie

;

Peau pathologie

;

Homme

;

Asie

;

Buschke Ollendorff syndrome

;

Adolescent

;

Etude cas

;

Dermatofibrose lenticulaire

;

Thaïlande

;

Ostéopoecilie

;

Naevus

;

Mots-clés espagnols / Spanish Keywords

Enfermedad hereditaria

;

Osteocondrodisplasia

;

Sistema osteoarticular patología

;

Piel patología

;

Hombre

;

Asia

;

Adolescente

;

Estudio caso

;

Dermatofibrosis lenticular

;

Tailandia

;

Osteopoiquilia

;

Nevo

;

Localisation / Location

INIST-CNRS, Cote INIST : 16224, 35400010501196.0090

Nº notice refdoc (ud4) : 13952909



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