Titre du document / Document title

Skoliose und Hüftbeugekontraktur bei Duchennescher Muskeldystrophie = Scoliosis and flexion contracture of the hip in Duchennes muscular dystrophy

Auteur(s) / Author(s)

FÜRDERER S. ⁽¹⁾ ; HOPF C. ⁽¹⁾ ; ZÖLLNER J. ⁽¹⁾ ; EYSEL P. ⁽¹⁾ ;

Affiliation(s) du ou des auteurs / Author(s) Affiliation(s)

⁽¹⁾ Orthopädische Klinik und Poliklinik der Johannes Gutenberg-Universität Mainz, ALLEMAGNE

Résumé / Abstract

Spinal deformity is common in muscular dystrophy and usually occurs after loss of walking ability. Unlike in idiopathic and other scoliosis forms, there seems to he no side preference of the convexity. Aim of the study was to analyse, if there is any relation between incidence and extent of walking ability, lower limb contractures and development of scoliosis. Methods: In a retrospective study, 45 patients with Duchenne muscular dystrophy who underwent surgery were analysed, concerning walking ability, contractures of lower extremities and scoliosis. Results: 1: No scoliosis was observed in ambulatory patients. 2: 96% of the wheelchair bound patients suffered from scoliosis. 3: 96% of the scoliosis patients had hip flexion or abduction contractures. 4: In 12 of 15 cases with side-different contractures, scoliosis tended to the side with the greater contracture. Conclusions: The influence of hip contracture and pelvic obliquity on scoliosis is discussed controversially. Concerning muscular dystrophy, there seems to be a positive correlation between convexity and hip contracture. If this is a causal relation or if there is a faster progression of structural alteration of the muscles on one side has to be further investigated.

Revue / Journal Title

Zeitschrift für Orthopädie und ihre Grenzgebiete   ISSN 0044-3220   CODEN ZOIGAP 

Source / Source

2000, vol. 138, n^o2, pp. 131-135 (34 ref.)

Langue / Language

Allemand

Editeur / Publisher

Thieme, Stuttgart, ALLEMAGNE  (1936) (Revue)

Mots-clés anglais / English Keywords

Duchenne muscular dystrophy ; Association ; Human ; Scoliosis ; Correlation analysis ; Symptomatology ; Contracture ; Hip ; Bending ; Spine ; Lower limb ; Nervous system diseases ; Neuromuscular diseases ; Genetic disease ; Diseases of the osteoarticular system ; Spine disease ; Deformation ; Striated muscle disease ;

Mots-clés français / French Keywords

Dystrophie musculaire progressive Duchenne ; Association ; Homme ; Scoliose ; Analyse corrélation ; Symptomatologie ; Contracture ; Hanche ; Flexion ; Rachis ; Membre inférieur ; Obliquité pelvienne ; Système nerveux pathologie ; Neuromusculaire pathologie ; Maladie héréditaire ; Système ostéoarticulaire pathologie ; Rachis pathologie ; Déformation ; Muscle strié pathologie ;

Mots-clés espagnols / Spanish Keywords

Distrofia muscular progresiva Duchenne ; Asociación ; Hombre ; Escoliosis ; Análisis correlación ; Sintomatología ; Contractura ; Cadera ; Flexión ; Raquis ; Miembro inferior ; Sistema nervioso patología ; Neuromuscular patología ; Enfermedad hereditaria ; Sistema osteoarticular patología ; Raquis patología ; Deformación ; Músculo estriado patología ;

Localisation / Location

INIST-CNRS, Cote INIST : 3853, 35400008756448.0070